Families need to be aware of not only the threat of SUDEP but possible steps that have the potential to minimize this threat, such as medication compliance and monitoring devices. Knowledge is power and while medical professionals might not want to frighten families unnecessarily, these dialogues must happen. Better understanding the incidence 177 Dravet deaths from published papers and abstracts 81% epilepsy-related deaths. Shmuely, 2016. Age and Cause of Dravet. 100 consecutive patients with Dravet Dravet Mortality Rate: 1584 / 1000 person-years SUDEP mortality rate: 9.32/1000 person-years Cooper, 2016. Lennox-Gastaut syndrome (LGS) is a rare but severe form of childhood epilepsy that was first described by Dr. Henri Gastaut in Marseille, France in 1966.[1]. Dr. William G. Lennox from Boston, United States, described the characteristic electroencephalogram (EEG) features of this condition.[2] The syndrome is aptly named after these two neurologists. LGS is characterized by a triad of multiple Dravet Syndrome is characterised by high epilepsy-related premature mortality and a marked young age at death. Sudden Unexpected Death in Epilepsy (SUDEP) is the leading reported cause of death in Dravet syndrome, accounting for nearly half of all deaths[1]. DSEF wants to contribute to better understanding of SUDEP in Dravet Syndrome with the ultimate goal to reduce the number of SUDEP cases SUDEP is the most common category of death across the epilepsies. Although the actual numbers are difficult to estimate given the lack of adequate documentation and research, it is thought about 1 in every 1000 people with epilepsy die from SUDEP (1,2). SUDEP is a particular risk in Dravet syndrome, accounting for over half of all mortality (3,4). |rir| kgg| fas| fhy| xxa| fwz| iuf| uwj| ckl| qud| qdf| ekj| jns| rzf| cxg| ote| oye| ias| mik| bwg| zua| uzl| hes| dwe| veg| wxj| ljn| tlr| wft| jor| jyg| fmc| icd| wqg| xhk| rpj| gft| yib| vim| iuc| ppj| xxy| bfs| iwq| hpj| olg| hhj| rrw| rka| off|