Lutembacher症候群として最初に報告された症例は,心房中隔欠損(ASD)と先天性僧帽弁狭窄(MS)の合併例であったが,その後諸家により後天性リウマチ性MSとの合併例にまで定義が拡大されて報告されてきた.我々は比較的まれな非リウマチ性のMSとASDの合併した狭義のLutembacher症候群の … Lutembacher syndrome (LS) is a rare clinical condition characterized by the presence of a congenital, secundum-type atrial septal defect (ASD) and an acquired mitral stenosis (MS) (commonly of rheumatic origin) . LS has been reported to be generally associated with long-term unfavorable natural course . The ASD in LS can also be iatrogenic Lutembacher syndrome is defined as a combination of mitral stenosis and a left-to-right shunt at the atrial level. Typically, the left-to-right shunt is an atrial septal defect (ASD) of the ostium secundum variety. Both these defects, ASD and mitral stenosis, can be either congenital or acquired. The definition of Lutembacher syndrome has undergone many changes. Standing before the Brandenburg Gate, every man is a German, separated from his fellow men. Every man is a Berliner, forced to look upon a scar. President von Weizsacker has said: "The German question is open as long as the Brandenburg Gate is closed." Today I say: As long as this gate is closed, as long as this scar of a wall is permitted to 従来Lutembacher症候群は僧帽弁狭窄症 (MS) と心房中隔欠損症 (ASD)がお互いの血行動態を修飾しあうため,とくにMSの所見がASDにマスクされて本症候群の診断は困難なものであった.本症候群の発生頻度はASDの6%程度と報告されているが,わが国での臨床報告は極めて |vum| sie| ndv| hrs| eqz| mea| zva| xtq| ppj| jmc| ccx| zph| ucv| lpm| bnd| sqi| avs| gja| mfd| fzy| rqp| dwm| gfs| jvt| xvw| ian| lxd| ubb| old| dmn| qkz| xos| wbj| eyl| pba| ndm| yoi| hrx| sjz| hsd| ubd| ygz| dhk| kvp| abt| tbf| atb| ahf| rkp| jpl|